Nursing Care Case Study: Sickle Cell
Disease
• A Case Presentation
• Prepared by: [Your Name]
• Date: [Presentation Date]
Socio-Demographic Data
• • Name: [Confidential]
• • Age: 10 years
• • Gender: Male
• • Weight: 26 kg
• • Residence: [Confidential]
• • Diagnosis: Sickle Cell Disease (SCD)
• • Hospital: Bugando Medical Centre
• • Date of Admission: 29 January 2025
• • Previous Medical History: SCD on folic acid &
Pathophysiology of Sickle Cell
Disease
• • Genetic disorder causing abnormal
hemoglobin (HbS)
• • Red blood cells become sickle-shaped
• • Leads to vaso-occlusion, anemia, and organ
damage
Impact on Mental Health
• • Chronic pain and hospitalizations lead to
anxiety and depression
• • Social withdrawal due to physical limitations
• • Stress for patient and family
Predisposing Factors
• • Genetic inheritance (autosomal recessive)
• • Hypoxia
• • Dehydration
• • Infections
• • Stress and cold exposure
Clinical Presentation (Literature vs.
Patient)
• • Literature: Pain, fever, anemia, jaundice,
breathlessness, fatigue
• • Patient: Shortness of breath, fever,
weakness, abdominal distention, pallor, spoon
nails
Investigations Required
• • Complete Blood Count (CBC)
• • Reticulocyte count
• • Peripheral smear
• • Hemoglobin electrophoresis
• • Liver/kidney function tests
• • Blood cultures
Patient's Investigations & Results
• • RBG: 10.1 mmol/L (admission), later 5.6
mmol/L
• • MRDT: Negative
Treatment Overview
• • Common treatments: Pain management, IV
fluids, antibiotics, blood transfusion
• • Patient received:
• - Paracetamol infusion
• - DNS & Sodium chloride IV
• - Sulbactam-Ceftriaxone
• - Ciprofloxacin
Nursing Care Plan: Identified Needs
• • Pain management
• • Hydration
• • Infection prevention
• • Nutritional support
• • Psychosocial support
Nursing Diagnoses
• 1. Acute pain related to vaso-occlusive crisis
• 2. Risk for infection due to
immunocompromised state
• 3. Imbalanced nutrition
• 4. Risk for delayed growth & development
Implementation & Evaluation
• • Pain: Paracetamol, monitoring
• • Hydration: IV fluids, oral intake
• • Infection: Antibiotics, monitoring
• • Nutrition: Dietary counseling
• • Psychosocial: Support & family involvement
Complications of SCD
• • Acute chest syndrome
• • Stroke
• • Severe anemia
• • Organ damage (kidneys, liver, spleen)
Complications in Patient
• • Moderate anemia (not critical)
• • No acute chest syndrome or stroke observed
Preventive Strategies
• • Hydration
• • Avoid extreme temperatures
• • Prompt infection treatment
• • Regular medication adherence
Prognosis & Family Involvement
• • Prognosis: Fair to good
• • Family educated on symptom management
& adherence to treatment
Holistic Nursing Role
• • Physical: Pain relief, hydration, infection
prevention
• • Psychosocial: Counseling, emotional support
• • Cultural: Respect for family beliefs
• • Spiritual: Support through counseling
Conclusion
• • SCD is a chronic, genetic disorder requiring
comprehensive management
• • Holistic nursing care improves outcomes
References
• • [Include relevant medical sources &
references]