Paralytic Squint Guidelines for Clinical Case Presentations
Anoop Thomas, Mythri HM, Mallipatna C Ashwin, Shamin Jacob
Types of cases:
Oculomotor Nerve Palsy
Trochlear Nerve Palsy
Abducent Nerve Palsy
History:
Presenting Complaints:
Diplopia
Pain
Drooping of Eyelid
Details: Causes of Ophthalmoplegia
Diplopia (ptosis may conceal diplopia) Congenital
Onset Traumatic
Unilateral or Bilateral Neoplastic
Vertical or Horizontal Demyelinating Disease
Worsening or Stationary Inflammatory
Diurnal Variation Ischaemic
Maximum in which field of gaze Toxic
Idiopathic
Pain
Onset and relationship with diplopia Painful Ophthalmoplegia:
Severity Intracranial Aneurysm
Localisation Cavernous Sinus Thrombosis
Orbital Apex Syndrome
Drooping of eye lid Tolosa Hunt Syndrome
Onset Orbital Cellulitis
Progression Pseudotumor of the Orbit
Diurnal Variation
Association with fatigue
Visual Complaints
s/o Cavernous Sinus Thrombosis: Redness, Proptosis
CNS History
Headache, Nausea, Vomiting (also: Neck rigidity)
Loss of consciousness, Convulsions
Focal Neurological Defects or TIA (Hemiparesis, Hemi-anaesthesia)
Aphasia, Visual Hallucinations
Ataxia, Dysarthria, Dysphagia
Past History Mimics of cranial nerve palsies:
Diabetes Mellitus, Hypertension 3rd Nerve and 4th Nerve:
Ischaemic Heart Disease, Rheumatic Heart Disease Thyroid Eye Disease
Trauma (head injury or orbital trauma) Myasthenia Gravis
Hearing Loss, Tinnitus, Ear Infection, Sinusitis, Epistaxis
Malignancies: Weight loss, Neck surgeries, Radiation therapy 6th Nerve:
Hyperthyroidism: Tremors, Palpitations, Insomnia Thyroid Eye Disease
Tuberculosis Myasthenia Gravis
Child birth (Pituitary Apoplexy) Medial Wall Blow-Out
Orbital Myositis
Personal History Convergence Spasm
Alcohol, Tobacco smoking Eso-Duanne’s Syndrome
IV Drug abuse Infantile Esotropia
Examination:
General Physical Examination
CNS Examination:
HMF, Cranial Nerves, Sensory, Motor – gait, power, reflexes, coordination
Ocular Examination:
Head posture: Past Pointing:
Head tilt This test indicates a recent onset.
Chin elevation Elicited by asking the patient to point
Face turn to an object with his finger while
viewing it through the paretic eye.
Ocular Posture: The patient will initially point further
General Ocular Inspection (Exo- or enophthalmos) than the object.
Hirschberg’s Test
* Important to look out for
Cover/Uncover test internuclear ophthalmoplegia and
o Tropia or Phoria other gaze palsies
o Concomitant or Incomitant (Primary and Secondary deviation)
o Nystagmus: type, jerky or pendular, direction, null point Diplopia Charting:
1. Maximum separation is in the
direction in which the muscle
Diplopia charting (Hess chart or Lees screen if possible)
acts the most
Park-Bielschowsky’s 3-step test for vertical deviation
2. The image that appears farthest
Detect cyclo-deviation (Double Maddox)
belongs to the deviating eye
3. The image is displaced in the
Ocular Examination
direction of the paralysed muscle
Visual Acuity (Best corrected for distance and near, Colour, Confrontation)
Watch for Pseudoptosis!
Lids Associated with hypotropia and can
o Palpebral fissures (equal, ptosis) be mistaken for ptosis of 3rd CN
Palsy.
Anterior Segment Examination (aniridia, coloboma, heterochromia, cataract)
Internal Ophthalmoplegia:
Pupil: direct and consensual (comment on near reflex if reaction to light is poor) Isolated involvement of
accomodation and pupillary reflex –
Fundus (Distant Direct Ophthalmoscopy, Direct and Indirect Ophthalmoscopy) occurs with botulism and diphtheria.
o Disc
Size, Shape, Margins, C/D ratio (Horizontal and Vertical) Pupil Sparing 3rd Nerve Palsy:
Neuro-retinal rim (colour and thinning, capillary count) Ischaemic mononeuropathy due to
Spontaneous Venous Pulsations diabetes mellitus, hypertension, etc.
Peripapillary defects, NFL defects (Medical 3rd Nerve Palsy)
o Retinal vessels, fundus periphery and macula Miosed Pupil in 3rd CN Palsy:
Associated Horner’s Syndrome
o Remember: Hutchinson’s Pupil in Evolution
Bruckner's Test
Fundus Torsion
Eccentric Fixation (Foveal, Parafoveal, Perifoveal)
4. Extraocular Movement Stages of a Paralytic Squint:
o Duction, Versions, Convergence (watch for inhibitional palsy) 1. Paresis of Muscle
o Saccadic Velocity 2. Overacting ipsilateral antagonist
3. Inhibitional Palsy: Underacting
5. Refraction
antagonist of contralateral synergist
Intraocular Pressure (Differential Tonometry for muscle restrictions) 4. Long standing cases: Comitance
(aka: spread of comitance)