Síndrome de la Cimitarra

Journal of Tropical Pediatrics, 2000

The American Journal of Cardiology, 1978

, aged 15 hours to 39 months, with total anomalous pulmonary venous drainage to (1) the coronary sinus (three infants), (2) the portal system (one infant), or (3) the superior vena cava (one infant) were studied. In addition, an infant with a secundum atria1 septal defect and a large coronary sinus due to persistence of the left superior vena cava was studied. Echocardiograms were performed on the same day as cardiac catheterization.

Postgraduate Medical Journal, 2013

Scimitar syndrome (or pulmonary veno-lobar syndrome) is a rare congenital cardiac condition characterised by abnormal pulmonary venous return from the right lung directly into the inferior vena cava. It can be associated with hypoplastic right lung, pulmonary artery hypoplasia and dextrocardia, among others. 1 2 There are complete and incomplete variations. In the complete form, classically, the right lung is hypoplastic and is supplied by a systemic arterial branch from the aorta with hypoplasia of the right pulmonary artery, resulting in an abnormal right heart border on imaging.

American Heart Journal, 1973

Congenital Heart Disease, 2009

We present a very rare cardiac lesion where we found a combination of abnormal pulmonary venous drainage and left-sided obstructive lesions. This case gives new insight into the complex malformation of the heart, raising questions about cardiac embryology and timing of interfering events. Here we describe the lesion for the first time and review the related literature. To the best of our knowledge, this combination has never been reported.

Monaldi archives for chest disease = Archivio Monaldi per le malattie del torace / Fondazione clinica del lavoro, IRCCS [and] Istituto di clinica tisiologica e malattie apparato respiratorio, Università di Napoli, Secondo ateneo, 2009

Over the years, different techniques have been introduced for the repair of sinus venosus atrial septal defect (ASD) with anomalous right-sided pulmonary venous connection to the superior vena cava. We report the case of a 9-year-old girl, who presented with dyspnea and peripheral cyanosis. Preoperative echocardiography and angiography findings suggested a partial anomalous pulmonary venous connection. On cardiopulmonary bypass, the ASD was dilated, and the anomalous pulmonary vein was anastomosed to the right atrium and redirected to the left atrium using an intraatrial baffle and a tube graft. The intraoperative and postoperative periods were uneventful, and the patient is currently in good health at 4.5 years' follow-up.

American Heart Journal, 1993

Clinical Cardiology, 2003

Radiology Case Reports, 2017

Clinical Radiology, 2002