Cystic Fibrosis Standards of Care, Australia
Dominic Fitzgerald
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Abstract
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This document details the standards of care for patients with cystic fibrosis (CF) in Australia. It outlines comprehensive inpatient and outpatient care protocols, management strategies for different age groups, and transition requirements for patients. Specific medical treatments, nutritional advice, and recommendations for lung transplantation and ongoing support for families are also discussed, emphasizing the importance of tailored healthcare strategies to address individual patient needs systematically.
Key takeaways
- The majority of adults with CF and parents of children with CF are in favour of CF specialist care .
- Cystic Fibrosis Clinic is defined as a service which provides care for patients with CF at a hospital which is close to the geographical location (home) of the patient and where the patients are also seen periodically by members of the CF specialist centre.
- There are 23 CF centres and CF clinics in Australia
- The local CF Association can be involved to help facilitate the process.
- Despite significant improvements in survival for people with cystic fibrosis (CF), more than 90% of patients die as a consequence of CF lung disease, with the majority dying in their 20s to 40s .
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338 Variability of clinical outcomes and impact of risk factors in cystic fibrosis (CF) patients in a regional CF center in a developing country
Journal of Cystic Fibrosis, 2011
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Respiratory Care and Cystic Fibrosis
Respiratory Care, 2009
The 43rd RESPIRATORY CARE Journal Conference brought together experts from the United States, Canada, and the United Kingdom to review the art and science of cystic fibrosis (CF). This is the first time that CF was the topic for the Journal Conference, and it came about 6 decades after the disease was named, and 20 years after the gene was discovered on chromosome 7. Though CF is a multisystem disease, it is the chronic and progressive lung disease that causes most of the morbidity and mortality. The participants at the conference reviewed the epidemiology, pathophysiology, treatment, and novel therapies in the pipeline for CF lung disease. They also emphasized the many crucial roles that the respiratory therapist plays in CF, including diagnostic testing, aerosol therapies, airway clearance, infection control, patient and peer education, and patient advocacy. The May and June 2009 issues of the Journal reflect how diligently the participants worked to provide up-to-date reviews and lively discussions of these topics.
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