Pancreatic insufficiency in Cystic Fibrosis
- PMID: 28986019
- DOI: 10.1016/j.jcf.2017.06.011
Pancreatic insufficiency in Cystic Fibrosis
Abstract
Pancreatic insufficiency (PI) affects about 85% of the cystic fibrosis population. Although most are PI soon after birth, some will have pancreatic sufficiency (PS) for some or all of their life. Understanding the clinical presentation, diagnosis, and management of PI is crucial to the care of people with cystic fibrosis.
Keywords: Fat soluble vitamins; Pancreas; Pancreatic enzyme therapy; Pancreatic insufficiency; Pancreatitis.
Copyright © 2017 European Cystic Fibrosis Society. Published by Elsevier B.V. All rights reserved.
Similar articles
-
[Physiopathology, diagnosis, and treatment of exocrine pancreatic insufficiency in patients with cystic fibrosis].Gastroenterol Hepatol. 2005 Feb;28 Suppl 1:29-32. doi: 10.1157/13071384. Gastroenterol Hepatol. 2005. PMID: 15899235 Spanish. No abstract available.
-
[Pancreatic infringement exocrine and endocrine in cystic fibrosis].Arch Pediatr. 2016 Dec;23(12S):12S21-12S32. doi: 10.1016/S0929-693X(17)30059-3. Arch Pediatr. 2016. PMID: 28231890 Review. French.
-
Exokrine Pankreasinsuffizienz.Ther Umsch. 2016 Nov;73(9):500-504. doi: 10.1024/0040-5930/a000825. Ther Umsch. 2016. PMID: 27805488 Review. German. No abstract available.
-
Pancreas and pancreatitis: Exocrine pancreatic insufficiency.Pediatr Pulmonol. 2024 Sep;59 Suppl 1:S44-S52. doi: 10.1002/ppul.27013. Pediatr Pulmonol. 2024. PMID: 39105352 Review.
-
Detection and follow up of exocrine pancreatic insufficiency in cystic fibrosis: a review.Eur J Pediatr. 2000 Aug;159(8):563-8. doi: 10.1007/s004310000507. Eur J Pediatr. 2000. PMID: 10968231 Review.
Cited by
-
Association between Dietary Intake and Faecal Microbiota in Children with Cystic Fibrosis.Nutrients. 2023 Dec 5;15(24):5013. doi: 10.3390/nu15245013. Nutrients. 2023. PMID: 38140272 Free PMC article.
-
The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review.Front Pediatr. 2022 Jun 27;10:914790. doi: 10.3389/fped.2022.914790. eCollection 2022. Front Pediatr. 2022. PMID: 35832587 Free PMC article. Review.
-
Exocrine pancreatic insufficiency: prevalence, diagnosis, and management.Clin Exp Gastroenterol. 2019 Mar 21;12:129-139. doi: 10.2147/CEG.S168266. eCollection 2019. Clin Exp Gastroenterol. 2019. PMID: 30962702 Free PMC article. Review.
-
Regulation of CFTR Biogenesis by the Proteostatic Network and Pharmacological Modulators.Int J Mol Sci. 2020 Jan 10;21(2):452. doi: 10.3390/ijms21020452. Int J Mol Sci. 2020. PMID: 31936842 Free PMC article. Review.
-
Genotype patterns for mutations of the cystic fibrosis transmembrane conductance regulator gene: a retrospective descriptive study from Saudi Arabia.Ann Saudi Med. 2020 Jan-Feb;40(1):15-24. doi: 10.5144/0256-4947.2020.15. Epub 2020 Feb 6. Ann Saudi Med. 2020. PMID: 32026723 Free PMC article.
Publication types
MeSH terms
LinkOut - more resources
Full Text Sources
Other Literature Sources
Medical
Research Materials
Miscellaneous